Vanishing aneurysms in Behcetâ€™s disease - A case series
BehÃ§etâ€™s disease is a systemic vasculitis with a wide spectrum of manifestations. Although pulmonary involvement is typical, the presence of pulmonary arterial aneurysms is associated with a high incidence of mortality and morbidity. We report two cases of BehÃ§etâ€™s disease with pulmonary arterial involvement who presented with hemoptysis, showed significant treatment response, thus, highlighting the importance of early diagnosis and therapeutic management.
BehÃ§et H. [Uber rezidivierende aphthose, durch ein virus verursachte Geschwure am Mund, am Auge und an den Genitalien].[Article in German]. Dermatol Woschensch. 1937;105:1152-7.
International Team for the Revision of the International Criteria for BehÃ§et's Disease (ITR-ICBD). The International Criteria for BehÃ§et's Disease (ICBD): a collaborative study of 27 countries on the sensitivity and specificity of the new criteria. J Eur Acad Dermatol Venereol 2014;28:338-47.
Nabih M, Naguib S, El Menyawi M, Ismail I. Pulmonary manifestations in a group of patients with BehÃ§etâ€²s disease. Egypt J Intern Med 2015;27:8.
Hiller N, Lieberman S, Chajek-Shaul T, et al. Thoracic manifestations of BehÃ§et disease at CT. RadioGraphics 2004;24:801â€“8.
Ceylan N, Bayraktaroglu S, Erturk SM, Savas R, Alper H. Pulmonary and vascular manifestations of BehÃ§et disease: Imaging findings. Am J Roentgenol 2010;194:W158-64.
Kang EH1, Kim JY, Takeuchi F, et al. Associations between the HLA-A polymorphism and the clinical manifestations of Behcets disease. Arthritis Res Ther 2011;13:R49.
Agha A, Bella AM, Assiri AH, Al-Hakami M. Can Behcet's disease related pulmonary arterial aneurysms be completely resolved? Open Rheumatol J 2011;5:88-90.
de Albuquerque Botura C, Bersani-Amado LE, Zacarias-JÃºnior AR, et al. BehÃ§etâ€™s disease: Pulmonary aneurysm resolution with oral therapy and HLA B72 allele association. Clin Med Res 2018;16:37-40.
Aktogu S, Erer OF, Urpek G, et al. Multiple pulmonary arterial aneurysms in Behcetâ€˜s disease: clinical and radiologic remission after cyclophosphamide and corticosteroid therapy. Respiration 2002;69:178-81.
Hamuryudan V, Yurdakul S, Moral F, et al. Pulmonary arterial aneurysms in BehÃ§etâ€™s syndrome: a report of 24 cases. Br J Rheumatol 1994;33:48-5.
- Abstract views: 289
- PDF: 123
PAGEPress has chosen to apply the Creative Commons Attribution NonCommercial 4.0 International License (CC BY-NC 4.0) to all manuscripts to be published.