Effects of an outpatient service holistic rehabilitation program in a case of pulmonary atresia


A 42-year-old woman affected by pulmonary atresia came to our attention complaining of dyspnea and fatigue for minimal efforts with important desaturation. After assessing her basal functional capacity with a cardiopulmonary exercise test, the patient was enrolled in an extremely individualized rehabilitation program, which entailed a discreet improvement in the quality of life indices, in the absence of side effects. This paper shows that even patients with extremely severe forms of congenital heart disease, when clinical stable, can undergone a tailored cardiorespiratory rehabilitation program. This must be carried out in a monitored environment and under the supervision of expert personnel.



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Cardiology - Case Reports
Pulmonary atresia, cardiorespiratory rehabilitation, cardiopulmonary exercise test
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How to Cite
Bussotti, M., Sommaruga, M., Krasinska, P., & Dalla Vecchia, L. A. (2021). Effects of an outpatient service holistic rehabilitation program in a case of pulmonary atresia. Monaldi Archives for Chest Disease, 91(1). https://doi.org/10.4081/monaldi.2021.1605