Exertional dyspnea and hemoptysis in an adolescent: is it tuberculosis only?



  • Nitin Goel | drnitingoel@gmail.com Department of Pulmonary Medicine, Vallabhbhai Patel Chest Institute, University of New Delhi, India. https://orcid.org/0000-0001-5155-8985
  • Nitesh Goyal Department of Pulmonary Medicine, Vallabhbhai Patel Chest Institute, University of New Delhi, India. https://orcid.org/0000-0003-1301-0526
  • Raj Kumar Department of Pulmonary Medicine, Vallabhbhai Patel Chest Institute, University of New Delhi, India.


Unilateral pulmonary artery atresia (UPAA), commonly detected in childhood, can occasionally present in adulthood with typical symptoms of recurrent pulmonary infections, dyspnoea on exertion and hemoptysis. An 18-year-old girl presented with complaints of cough, dyspnea on exertion and hemoptysis. Chest radiograph revealed dilated pulmonary trunk, signs of left sided volume loss and cavitating lesion in left lower zone. Pulmonary CT angiography found left pulmonary artery atresia. Endobronchial lung biopsy revealed granulomatous inflammation. Diagnosis of left sided UPAA with pulmonary tuberculosis was established. She responded well to the anti-tubercular therapy. This case highlights the importance of awareness about UPAA as a possible differential for exertional dyspnea, recurrent chest infections, hemoptysis and pulmonary hypertension in adults.



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Pneumology - Case Reports
Pulmonary atresia, pulmonary hypertension, computed tomography angiography
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How to Cite
Goel, Nitin, Nitesh Goyal, and Raj Kumar. 2021. “Exertional Dyspnea and Hemoptysis in an Adolescent: Is It Tuberculosis Only?”. Monaldi Archives for Chest Disease 91 (1). https://doi.org/10.4081/monaldi.2021.1613.

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