The challenging management of a giant intrathoracic desmoid tumour: a case report

https://doi.org/10.4081/monaldi.2021.1702

Authors

  • Christos Kakos | kakoschristos91@gmail.com Royal Victoria Hospital, Belfast, United Kingdom, United Kingdom. https://orcid.org/0000-0003-0614-0349
  • Savvas Lampridis Department of Thoracic Surgery, University College London Hospitals NHS Foundation Trust, London, United Kingdom, Greece. https://orcid.org/0000-0003-2827-5826
  • Georgios Geropoulos Department of Thoracic Surgery, University College London Hospitals NHS Foundation Trust, London, United Kingdom, United Kingdom. https://orcid.org/0000-0002-2066-7975
  • Reena Khiroya Department of Histopathology, University College London Hospitals NHS Foundation Trust, London, United Kingdom, United Kingdom.
  • Achilleas Antonopoulos Department of Thoracic Surgery, University College London Hospitals NHS Foundation Trust, London, United Kingdom, Greece.
  • Sofoklis Mitsos Department of Thoracic Surgery, University College London Hospitals NHS Foundation Trust, London, United Kingdom, United Kingdom. https://orcid.org/0000-0002-0606-7287
  • Nikolaos Panagiotopoulos Department of Thoracic Surgery, University College London Hospitals NHS Foundation Trust, London, United Kingdom, United Kingdom.

Abstract

Desmoid tumours are rare, locally aggressive neoplasms exhibiting high tendency for recurrence, even after complete resection. Only 1 in 5 of them originates from the chest wall, usually measuring less than 10 cm at diagnosis. Herein, we report the case of a woman presenting with symptoms of gradual lung compression by a giant desmoid tumour occupying the entire hemithorax. She underwent complete surgical resection of the tumour and chest wall reconstruction. She had disease recurrence 15 months later and currently remains under regular follow-up. The management of intrathoracic desmoid tumours is challenging because they are usually not diagnosed until they become large enough to cause compression symptoms. While medical management is the primary modality of treatment, surgery could be considered in selected cases where significant symptoms arise, and the functional status is impaired secondary to the tumour. Adjuvant radiotherapy to minimise the risk of local recurrence should also be considered.

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Published
2021-03-08
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Issue
Section
Pneumology - Case Reports
Keywords:
desmoid tumour, desmoid-type fibromatosis, aggressive fibromatosis, intrathoracic, case report
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How to Cite
Kakos, Christos, Savvas Lampridis, Georgios Geropoulos, Reena Khiroya, Achilleas Antonopoulos, Sofoklis Mitsos, and Nikolaos Panagiotopoulos. 2021. “The Challenging Management of a Giant Intrathoracic Desmoid Tumour: A Case Report”. Monaldi Archives for Chest Disease, March. https://doi.org/10.4081/monaldi.2021.1702.

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