A case of arrhythmogenic right ventricular cardiomyopathy with biventricular involvement

https://doi.org/10.4081/monaldi.2019.1009

Authors

  • Filippo Brandimarte | brandimarte.filippo@gmail.com San Giovanni Addolorata Community Hospital, Cardiology and Rehabilitation Unit, Department of Medicine, Rome, Italy.
  • Alessandro Battagliese San Giovanni Addolorata Community Hospital, Cardiology and Rehabilitation Unit, Department of Medicine, Rome, Italy.
  • Silvana Petronilla Pirillo San Giovanni Addolorata Community Hospital, Department of Radiology, Rome, Italy.
  • Maria Teresa Mallus San Giovanni Addolorata Community Hospital, CCU and Interventional Cardiology, Department of Emergency, Rome, Italy.
  • Rosa Maria Manfredi San Giovanni Addolorata Community Hospital, CCU and Interventional Cardiology, Department of Emergency, Rome, Italy.
  • Giovanni Carreras San Giovanni Addolorata Community Hospital, Cardiology and Rehabilitation Unit, Department of Medicine, Rome, Italy.

Abstract

We reported a case of a young adult male aged 18 years admitted in our institution for syncope during a basketball match. No previous symptoms were reported. Electrocardiogram (ECG) showed T-wave inversion in the anterior leads and an incomplete right bundle branch block. Surprisingly, a complete echocardiographic evaluation demonstrated the presence of severe right ventricular enlargement with significant wall motion abnormalities, apical aneurysm and reduced systolic function. Cardiac Magnetic Resonance was pathognomonic for a fibro-fatty replacement of both ventricles. We decided for a subcutaneous defibrillator implantation and, after inducing a ventricular fibrillation to test the device status, epsilon wave appeared on the ECG. This clinical scenario depicted an advanced arrhythmogenic right ventricular cardiomyopathy at its first clinical manifestation.

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Published
2019-03-27
Info
Issue
Section
Cardiology - Case Reports
Keywords:
Syncope, Arrhythmogenic right ventricular dysplasia, sudden death
Statistics
  • Abstract views: 644

  • PDF: 482
How to Cite
Brandimarte, Filippo, Alessandro Battagliese, Silvana Petronilla Pirillo, Maria Teresa Mallus, Rosa Maria Manfredi, and Giovanni Carreras. 2019. “A Case of Arrhythmogenic Right Ventricular Cardiomyopathy With Biventricular Involvement”. Monaldi Archives for Chest Disease 89 (1). https://doi.org/10.4081/monaldi.2019.1009.