https://doi.org/10.4081/monaldi.2021.1709
Pulmonary alveolar microlithiasis: Blizzard of lung
Submitted: December 1, 2020
Accepted: April 22, 2021
Published: June 10, 2021
Accepted: April 22, 2021
Abstract Views: 1539
PDF: 671
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Authors
Pulmonary alveolar microlithiasis (PAM) is a rare inherited disorder in which patients present with either nonspecific signs and symptoms or are asymptomatic. Clinical-radiological dissociation is a commonly seen feature of the disease. Majority of cases are diagnosed in second and third decade of life, although presentation in paediatric and elderly population is also reported. Pathognomonic radiological findings, with normal calcium and phosphate levels can confirm the diagnosis without the need of further investigations in large number of cases. A high index of suspicion and knowledge of the disease is of paramount importance as it has a wide range of presentation and variable course thus posing a diagnostic challenge. We present two cases of this rare disease in elderly females with distinct presentations although with similar and characteristic radiological findings along with a brief review of literature of the disease.
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How to Cite
Mittal, Richa, Rohit Kumar, Juvva Kishan Srikanth, Siddharth Raj Yadav, Ravi Chandak, and Shibdas Chakrabarti. 2021. “Pulmonary Alveolar Microlithiasis: Blizzard of Lung”. Monaldi Archives for Chest Disease 91 (4). https://doi.org/10.4081/monaldi.2021.1709.
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