https://doi.org/10.4081/monaldi.2021.1874
A rare cause of bilateral pleural effusion – desmoplastic small round cell tumor
Submitted: April 1, 2021
Accepted: October 6, 2021
Published: November 16, 2021
Accepted: October 6, 2021
Abstract Views: 1126
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Authors
Desmoplastic small round cell tumor (DSRCT) is a rare, extremely aggressive and malignant tumor predominantly affects young adolescent males and typically presents as a large intra-abdominal mass. However, tumor arising from other body sites are also reported in the literature. Histology and immunohistochemistry play an important role in the diagnosis and differentiating this rare tumor from other round cell tumors. A multidisciplinary approach consisting of a combination of surgery, chemotherapy and radiation therapy is the treatment of choice as there is no standard therapy. We report a case of DSRCT of pleura presenting as bilateral pleural effusion in a young adolescent male who was treated with both surgery and chemotherapy. However, the patient succumbed to illness after one year of diagnosis.
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As the corresponding author I have all the rights to make necessary changes as per the request of the journalHow to Cite
Baburao, Archana, Poonam Maurya, Amulya Chakenahalli, and Huliraj Narayanswamy. 2021. “A Rare Cause of Bilateral Pleural Effusion – Desmoplastic Small Round Cell Tumor ”. Monaldi Archives for Chest Disease 92 (2). https://doi.org/10.4081/monaldi.2021.1874.
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