https://doi.org/10.4081/monaldi.2022.2342

Bronchiectasis without lower respiratory symptoms in the presence of multisystem anomalies – a clinical clue to diagnose esophageal lung anomaly

Vol. 93 No. 1 (2023)
Submitted: June 2, 2022
Accepted: June 27, 2022
Published: July 4, 2022
Esophageal lung, communicating bronchopulmonary foregut malformations, bronchiectasis, pneumonectomy
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Authors

Amit Gupta
amitpedsurgeon@gmail.com
https://orcid.org/0000-0001-7869-2818
Department of Pediatric Surgery, All India Institute of Medical Sciences, Bhopal, India.
Aman Snehil
https://orcid.org/0000-0003-2291-7082
Department of Radiodiagnosis, All India Institute of Medical Sciences, Bhopal, India.
Sujeet Kumar
Department of Pediatric Surgery, All India Institute of Medical Sciences, Bhopal, India.
Roshan Chanchlani
https://orcid.org/0000-0002-8086-9376
Department of Pediatric Surgery, All India Institute of Medical Sciences, Bhopal, India.
Reyaz Ahmad
https://orcid.org/0000-0002-2855-6321
Department of Pediatric Surgery, All India Institute of Medical Sciences, Bhopal, India.
Keerti Swarnkar
https://orcid.org/0000-0002-8319-1476
Department of Pediatrics, All India Institute of Medical Sciences, Bhopal, India.
Garima Goel
Department of Pathology, All India Institute of Medical Sciences, Bhopal, India.

Esophageal lung is a type of Group-II communicating bronchopulmonary foregut malformations (CBPFM) usually diagnosed beyond neonatal period during investigation for recurrent respiratory symptoms and persistent radiographic features suggesting pneumonia or bronchiectasis. In our case, we noticed bronchiectasis and disproportionately severe volume loss in an infant with associated multisystem anomalies in the absence of “significant” lower respiratory tract symptoms. A detailed evaluation with repeat imaging confirmed a Group-II CBPFM, a congenital pathology instead of an infective cause. Pneumonectomy is a more prudent option instead of undertaking major airway reconstruction for the dysplastic “dysfunctional” tissue. Amongst the various associated anomalies reported till now, the associated rib and renal anomalies noted by us have not been described earlier to the best of our knowledge.

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How to Cite

Gupta, Amit, Aman Snehil, Sujeet Kumar, Roshan Chanchlani, Reyaz Ahmad, Keerti Swarnkar, and Garima Goel. 2022. “Bronchiectasis Without Lower Respiratory Symptoms in the Presence of Multisystem Anomalies – a Clinical Clue to Diagnose Esophageal Lung Anomaly”. Monaldi Archives for Chest Disease 93 (1). https://doi.org/10.4081/monaldi.2022.2342.
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